Radiology imaging “Agenesis of the Portal Vein”

Hypoplasia or agenesis of the portal vein may be secondary to excessive obliteration of the primitive hepatic or vitelline sinusoids to the venae advehentes, which later become intrahepatic branches of the portal vein or to perinatal thrombosis of the portal vein. Associated nodular hyperplasia, hepatic adenoma, or hepatocellular carcinoma in the ischemic liver due to poor portal venous supply may be clinically important (Fig. radiology imaging in bellow).

“radiology imaging Hepatocellular carcinoma” (ruptured) associated with agenesis of the portal vein.
A 12-year-old female presented with shock and intraperitoneal bloody ascites.
(a and b) Enhanced CT shows a large hepatic tumor (arrows) with subcapsular hematoma and bloody ascites (open arrows). A small superior mesenteric vein (curved arrow) empties into the porta hepatis without opacification of the portal vein (PV) and intrahepatic branches (arrowheads). An enlarged left renal vein and IVC are noted.
(c) “radiology interventional” of Transarterial portography reveals hypogenesis of the portal vein (arrows) and collateral circulation of mesenteric blood flow to the IVC via mesenteric–gonadal venous anastomosis (curved arrows). Autopsy proved ruptured hepatocellular carcinoma

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